Narrowband UVB phototherapy in erythropoietic protoporphyria: case series

M. Sivaramakrishnan; J. Woods; R. Dawe

doi:10.1111/bjd.12714

Narrowband UVB phototherapy in erythropoietic protoporphyria: case series

M. Sivaramakrishnan, J. Woods, R. Dawe

Research output: Contribution to journal › Article › peer-review

21 Citations (Scopus)

Abstract

Erythropoietic protoporphyria (EPP) is an inherited disorder of the haem metabolic pathway. It causes disabling cutaneous photosensitivity and, sometimes liver disease due to the accumulation of protoporphyrin in blood, liver and other tissues.(1) Holme SA et al reported the median age at onset and diagnosis in patients with EPP in the UK as 1 and 12 years respectively, with diagnosis being delayed until the age of 20 years or more in 34% of their patients.(2) However, late presentation of EPP in adults has been reported.(3) This article is protected by copyright. All rights reserved.

Original language	English
Journal	British Journal of Dermatology
Early online date	1 Nov 2013
DOIs	https://doi.org/10.1111/bjd.12714
Publication status	Published - 2013

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title = "Narrowband UVB phototherapy in erythropoietic protoporphyria: case series",

abstract = "Erythropoietic protoporphyria (EPP) is an inherited disorder of the haem metabolic pathway. It causes disabling cutaneous photosensitivity and, sometimes liver disease due to the accumulation of protoporphyrin in blood, liver and other tissues.(1) Holme SA et al reported the median age at onset and diagnosis in patients with EPP in the UK as 1 and 12 years respectively, with diagnosis being delayed until the age of 20 years or more in 34% of their patients.(2) However, late presentation of EPP in adults has been reported.(3) This article is protected by copyright. All rights reserved.",

author = "M. Sivaramakrishnan and J. Woods and R. Dawe",

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AU - Woods, J.

AU - Dawe, R.

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N2 - Erythropoietic protoporphyria (EPP) is an inherited disorder of the haem metabolic pathway. It causes disabling cutaneous photosensitivity and, sometimes liver disease due to the accumulation of protoporphyrin in blood, liver and other tissues.(1) Holme SA et al reported the median age at onset and diagnosis in patients with EPP in the UK as 1 and 12 years respectively, with diagnosis being delayed until the age of 20 years or more in 34% of their patients.(2) However, late presentation of EPP in adults has been reported.(3) This article is protected by copyright. All rights reserved.

AB - Erythropoietic protoporphyria (EPP) is an inherited disorder of the haem metabolic pathway. It causes disabling cutaneous photosensitivity and, sometimes liver disease due to the accumulation of protoporphyrin in blood, liver and other tissues.(1) Holme SA et al reported the median age at onset and diagnosis in patients with EPP in the UK as 1 and 12 years respectively, with diagnosis being delayed until the age of 20 years or more in 34% of their patients.(2) However, late presentation of EPP in adults has been reported.(3) This article is protected by copyright. All rights reserved.

U2 - 10.1111/bjd.12714

DO - 10.1111/bjd.12714

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SN - 0007-0963

JO - British Journal of Dermatology

JF - British Journal of Dermatology

ER -

Narrowband UVB phototherapy in erythropoietic protoporphyria: case series

Abstract

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